Ackerman syndrome

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Ackerman syndrome
Other namesPyramidal molar-glaucoma-upper abnormal lip syndrome, interstitial granulomatous dermatitis with arthritis (IGDA)
Ackerman syndrome is inherited in an autosomal recessive manner

Ackerman syndrome or interstitial granulomatous dermatitis is a familial syndrome of fused molar roots with a single canal (taurodontism), hypotrichosis, full upper lip without a cupid's bow, thickened and wide philtrum, and occasional juvenile glaucoma.[1][2][3] It was described by James L. Ackerman, A. Leon Ackerman, and A. Bernard Ackerman.[4]

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